-
Alternative name
Alpha galactosidase A, galactosidase, alpha antibody
-
Catalog
A000329
-
Size100μg
-
Formliquid
-
Purity≥95% as determined by SDS-PAGE
-
StoragePBS with 0.02% sodium azide and 50% glycerol pH 7.3 , -20℃ for 24 months (Avoid repeated freeze / thaw cycles.)
-
ClonalityPolyclonal Antibody
-
Host Rabbit
-
Species ReactivityHuman,Mouse ,Rat
-
Applications Tested/SuitableELISA,WB,IF
-
PurificationImmunogen affinity purified
-
Immunogengalactosidase, alpha
-
Western BlotHEK-293 cells were subjected to SDS PAGE followed by western blot with A000329(GLA antibody) at dilution of 1:1500
-
Recommended dilutionWB :1:500-1:5000;IF:1:10-1:100
-
Product Description specificalGLA, also named as Melibiase, Agalsidas and Alpha-galactosidase A, Belongs to the glycosyl hydrolase 27 family. It hydrolysis of terminal, non-reducing alpha-D-galactose residues in alpha-D-galactosides, including galactose oligosaccharides, galactomannans and galactolipids. Fabry disease is an X-linked lysosomal storage disorder resulting from the deficient activity of GLA. Enzyme replacement therapy (ERT) with GLA is currently the most effective therapeutic strategy for patients with Fabry disease, a lysosomal storage disease.
-
Gene nameGLA
-
locationLysosome
-
Uniprot IDP06280
-
Calculated M.W.49kDa
-
Observed M.W.49 kDa
-